Management of a Pediatric Patient With a Left Ventricular Assist Device and Symptomatic Acquired von Willebrand Syndrome Presenting for Orthotopic Heart Transplant. (December 2020)

• Record Type: Journal Article
• Authors: Flannery, Kaitlin M; Kamra, Komal; Maeda, Katsuhide; Shuttleworth, Paul; Almond, Christopher; Navaratnam, Manchula
• Is Part Of: Seminars in cardiothoracic and vascular anesthesia. Volume 24:Number 4(2020)
• Page Start: 355
• Page End: 359
• Publication Date: 2020-12
• Subjects: coagulopathy -- acquired von Willebrand syndrome -- ventricular assist devices -- orthotopic heart transplant -- cardiopulmonary bypass; Cardiovascular system -- Surgery -- Methods -- Periodicals; Chest -- Surgery -- Methods -- Periodicals; Anesthesia -- Periodicals; Anesthetics -- Periodicals; Anesthesia -- Periodicals; Anesthetics -- Periodicals; Cardiovascular Surgical Procedures -- methods -- Periodicals; Thoracic Surgical Procedures -- methods -- Periodicals; 617.96
• DOI: 10.1177/1089253220949386
• Languages: English
• ISSNs: 1089-2532

Abstract

We present the successful perioperative management of an 11-year-old patient presenting for heart transplant with a left ventricular assist device, symptomatic acquired von Willebrand syndrome, and recent preoperative intracranial hemorrhage. A brief review of the pathophysiology of acquired von Willebrand syndrome is included. As the number of pediatric patients supported with ventricular assist devices continues to increase, the management of symptomatic acquired von Willebrand syndrome during the perioperative period is an important consideration for anesthesiologists.