Disease recurrence after lung transplantation for idiopathic pulmonary hemosiderosis. (2020)

• Record Type: Journal Article
• Authors: Ross, Bryan; Halloran, Kieran; Adam, Benjamin; Laing, Bryce; Hirji, Alim
• Is Part Of: Respiratory medicine case reports. Volume 30(2020)
• Publication Date: 2020
• Subjects: Idiopathic pulmonary hemosiderosis -- Pulmonary hypertension -- Lung transplant -- Hemoptysis -- Disease recurrence; Respiratory organs -- Diseases -- Periodicals; Chest -- Diseases -- Periodicals; Respiratory Tract Diseases -- Periodicals; Respiratory System -- Periodicals; Chest -- Diseases; Respiratory organs -- Diseases; Electronic journals; Periodicals; 616.2
• DOI: 10.1016/j.rmcr.2020.101128
• Languages: English
• ISSNs: 2213-0071

Abstract

Abstract: Idiopathic pulmonary hemosiderosis is characterized by the triad of hemoptysis, iron deficiency anemia and pulmonary infiltrates. Though idiopathic pulmonary hemosiderosis has classically been described as a childhood disease, survival into adulthood is possible. Treatment options for advanced and/or refractory disease is limited, and in our unique case of idiopathic pulmonary hemosiderosis with precapillary pulmonary hypertension, lung transplantation has had a favorable short-term outcome. We also demonstrate that disease recurrence of idiopathic pulmonary hemosiderosis following lung transplantation is possible.