"Chorea": A Unique Presentation of Left Atrial Myxoma in a Pediatric Patient. Issue 4 (July 2020)

• Record Type: Journal Article
• Authors: Chikkabyrappa, Sathish M.; Tretter, Justin T.; Vishwanath, Vijay; Bhatla, Puneet
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 11:Issue 4(2020)
• Page Start: NP11
• Page End: NP13
• Publication Date: 2020-07
• Subjects: myxoma -- chorea -- weakness; Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135117690109
• Languages: English
• ISSNs: 2150-1351

Abstract

We report an unusual presentation of a large left atrial myxoma in an eight-year-old girl who presented with the sudden onset of chorea. This case illustrates the fact that the presentation of chorea in nonendemic areas for rheumatic fever should raise suspicion for a myxoma. The chorea resolved soon after removal of the myxoma, supporting the hypothesis of an immune-mediated mechanism, or manifestation of paraneoplastic syndrome secondary to the myxoma.