Extra-axial chordoma of the gingiva. Issue 2 (April 2020)

• Record Type: Journal Article
• Authors: Ueda, Tsutomu; Kubota, Kazunori; Shiroma, Noriyuki; Maeda, Shogo; Furuie, Hiromi; Taruya, Takayuki; Hamamoto, Takao; Takeno, Sachio
• Is Part Of: Auris nasus larynx. Volume 47:Issue 2(2020)
• Page Start: 299
• Page End: 304
• Publication Date: 2020-04
• Subjects: 3D three-dimensional -- CK cytokeratin -- CT computed tomography -- MRI magnetic resonance images -- FDG fluorodeoxyglucose; Extra-axial chordoma -- Brachyury -- Three-dimensional model -- Surgical resection -- Bone tumour; Otolaryngology -- Periodicals; Electronic journals; 616
• DOI: 10.1016/j.anl.2019.03.005
• Languages: English
• ISSNs: 0385-8146

Abstract

Abstract: Background: Extra-axial chordomas are exceedingly rare malignant tumours. Herein, we present the first case of an extra-axial chordoma in the gingivae. Methods and results: A 21-year-old man presented with a suspected chordoma in the upper right gingiva. Diagnosis was difficult; however, owing to strong expression of the chordoma marker brachyury, extra-axial chordoma was ultimately diagnosed. The tumour was completely resected without performing a facial incision. To ensure its safety and effectiveness, the surgical procedure was simulated several times before its performance using a three-dimensional (3D) model. Twenty-four months after surgery, the patient remains disease-free. Conclusion: A diagnosis of extra-axial chordoma can be confirmed by immunohistochemical staining for brachyury.