Successful management of fibrosing mediastinitis with severe vascular compromise: Report of two cases and literature review. (2020)

• Record Type: Journal Article
• Authors: Argueta, Franklin; Villafuerte, David; Castaneda-Nerio, Jose; Peters, Jay; Restrepo, Carlos
• Is Part Of: Respiratory medicine case reports. Volume 29(2020)
• Publication Date: 2020
• Subjects: Fibrosing mediastinits -- Pulmonary artery stenosis -- Pulmonary hypertension; Respiratory organs -- Diseases -- Periodicals; Chest -- Diseases -- Periodicals; Respiratory Tract Diseases -- Periodicals; Respiratory System -- Periodicals; Chest -- Diseases; Respiratory organs -- Diseases; Electronic journals; Periodicals; 616.2
• DOI: 10.1016/j.rmcr.2019.100987
• Languages: English
• ISSNs: 2213-0071

Abstract

Abstract: Fibrosing mediastinitis is a rare disorder characterized by the invasive proliferation of fibrous tissue within the mediastinum. This fibrosis can result in compression of intrathoracic structures including the pulmonary vasculature leading to clinical symptoms and complications like pulmonary hypertension. Here, we present two cases of young patients with fibrosing mediastinitis complicated by pulmonary artery stenosis requiring medical and endovascular management with excellent results.