P1330 A rare coronary anomaly in the adult: an extremely large arteriovenous fistula. (17th January 2020)

• Record Type: Journal Article
• Authors: Garcia Bras, P; Cacela, D; Moura Branco, L; Ramos, R; Vaz Ferreira, V; Castelo, A; Branco Mano, T; Ilhao Moreira, R; Ferreira, R C
• Is Part Of: European heart journal. Volume 21(2020)Supplement 1
• Publication Date: 2020-01-17
• Subjects: Cardiovascular system -- Imaging -- Periodicals; Heart -- Imaging -- Periodicals; 616.10754
• DOI: 10.1093/ehjci/jez319.769
• Languages: English
• ISSNs: 2047-2404

Abstract

Abstract: Introduction: Arteriovenous coronary fistulae are a rare coronary anomaly, which can be congenital or acquired. They can be diagnosed in older adults with heart failure symptoms, atherosclerosis or cardiac arrhythmias. The authors report the case of an adult patient with an extremely large coronary artery fistula of the left main coronary artery (LMCA). Clinical case: A 57-year-old caucasian male with known background of arterial hypertension, obesity, pulmonary emphysema and bronchiectasis presented to a Cardiology outpatient appointment with symptoms of congestive heart failure and new-onset atrial fibrillation. A transthoracic echocardiogram was performed which revealed a possible coronary fistula with multiple rosary-like folds between the LMCA and the coronary sinus. Other echocardiographic findings were left ventricular and biatrial enlargement with biventricular systolic dysfunction (left ventricular ejection fraction 44%) and a GLS of -7.8% as well as mild pericardial effusion. The patient was referred to our hospital for further diagnostic work-up and clarification of the coronary anatomy. A cardiac computed tomography (CT) scan was done which showed ectasia and calcification of the LMCA, left anterior descending and circumflex arteries and a large caliber tortuous coronary fistula between the LMCA, the right atrium and the coronary sinus comprised of multiple folds covering from the pulmonary artery to the left atrium. A coronary artery angiography was also performed, which confirmed the detailed anatomy and dimensions of the coronary fistula. Follow-up magnetic resonance imaging revealed dilation of both left and right cardiac chambers with no significant shunt (QP/QS = 1) The patient was started on heart failure medical therapy and was referred to the Cardiac Surgery Department and is currently asymptomatic awaiting for surgical correction of the coronary fistula.