Non-Neural (S-100 Negative) Bronchial Granular Cell Tumor Causing Acute Respiratory Failure. (2nd January 2020)

• Record Type: Journal Article
• Authors: Chen, Stephanie Y; Sadanand, Arhanti; Dillon, Patrick A; He, Mai; Dehner, Louis P; Leonard, David S
• Is Part Of: Fetal and pediatric pathology. Volume 39:Number 1(2020)
• Page Start: 85
• Page End: 89
• Publication Date: 2020-01-02
• Subjects: endobronchial mass -- granular cell tumor -- S-100 protein -- alveolar soft part sarcoma; Pathology, Molecular -- Periodicals; Pediatrics -- Periodicals; Molecular biology -- Periodicals; Pediatric pathology -- Periodicals; Fetal Diseases -- pathology -- Periodicals; Infant, Newborn, Diseases -- pathology -- Periodicals; Pediatrics -- Periodicals; 618.92007
• DOI: 10.1080/15513815.2019.1636431
• Languages: English
• ISSNs: 1551-3815

Abstract

Abstract: Introduction : Endobronchial granular cell tumors are uncommon in the pediatric population. Case report : A 9-year-old female presented with respiratory failure due to an endobronchial tumor. After debulking and diagnosis, she underwent thoracotomy with right upper lobe resection and bronchoplasty. Pathology demonstrated an endobronchial S-100 negative granular cell tumor, which to our knowledge, is the first such report in the literature. Conclusion : Endobronchial granular cell tumors may cause obstructive respiratory failure, are amenable to surgery, and may be S-100 negative.