Carinal Resection and Reconstruction for an Obstructing Inflammatory Myofibroblastic Tumor in a Child. Issue 2 (March 2020)

• Record Type: Journal Article
• Authors: Nawalaniec, James; Mullapudi, Bhargava; Jiang, Wen; Brigger, Matthew; El-Said, Howaida; Saenz, Nicholas; Murthy, Raghav
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 11:Issue 2(2020)
• Page Start: 226
• Page End: 228
• Publication Date: 2020-03
• Subjects: Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135119837202
• Languages: English
• ISSNs: 2150-1351

Abstract

Inflammatory myofibroblastic tumor (IMT) is a rare soft tissue tumor characterized by proliferation of fibroblastic cells associated with an inflammatory infiltrate. Inflammatory myofibroblastic tumors have a predilection for the pediatric population and are usually found in the lung parenchyma but rarely at the carina. They rarely metastasize but can be locally destructive. Surgical resection is the cornerstone of therapy, which results in excellent survival despite risk of local recurrence. We present the case of a nine-year-old girl with an IMT mass at the carina and obstructing the left main stem bronchus, requiring extensive resection and reconstruction.