Grisel syndrome, sigmoid sinus thrombosis and rheumatic carditis: Case report of a rare association. (February 2020)

• Record Type: Journal Article
• Authors: Cucuzza, Maria Elena; D'Ambra, Angela; Evola, Francesco Roberto; Greco, Filippo; Smilari, Pierluigi
• Is Part Of: International journal of pediatric otorhinolaryngology. Volume 129(2020:Feb.)
• Publication Date: 2020-02
• Subjects: Grisel's syndrome -- Subluxation cervical joints -- Rheumatic carditis -- Cerebral venous thrombosis; Otolaryngology -- Periodicals; Pediatrics -- Periodicals; Otolaryngology -- Periodicals; Pediatrics -- Periodicals; Oto-rhino-laryngologie -- Périodiques; Pédiatrie -- Périodiques; 618.9209751
• DOI: 10.1016/j.ijporl.2019.109774
• Languages: English
• ISSNs: 0165-5876

Abstract

Abstract: Grisel's syndrome (GS) is a non traumatic atlanto-axial rotatory subluxation of C1–C2 joint. A six year old girl, 20 days after an episode of fever, developed a torticollis and a 3/6 heart murmur. The echocardiography showed a Rheumatic Carditis. The Brain and cervical spine Magnetic resonance imaging (MRI) and the Computerized Tomography (CT) showed rotary dislocation of C1–C2 vertebrae, compatible with GS, and cerebral venous thrombosis (CVT). An antibiotic therapy, Prednisone and a low molecular weight heparin for 7 days was prescribedfollowed by an oral anticoagulant for 6 months. After a month the MRI showed a reduction of the dislocation and cerebral venous recanalization.