Congenital Portosystemic Shunts: Current Diagnosis and Management. Issue 5 (May 2019)

• Record Type: Journal Article
• Authors: McLin, Valérie A.; Franchi Abella, Stephanie; Debray, Dominique; Guérin, Florent; Beghetti, Maurice; Savale, Laurent; Wildhaber, Barbara E.; Gonzales, Emmanuel
• Is Part Of: Journal of pediatric gastroenterology and nutrition. Volume 68:Issue 5(2019)
• Publication Date: 2019-05
• Subjects: congenital portosystemic shunts -- hepatopulmonary syndrome -- liver nodules -- neurocognitive delay -- occlusion test -- portopulmonary hypertension; Children -- Nutrition -- Periodicals; Pediatric gastroenterology -- Periodicals; Infants -- Nutrition -- Periodicals; Nutrition disorders in children -- Periodicals; Child Nutrition -- Periodicals; Digestive System -- growth & development -- Periodicals; Gastrointestinal Diseases -- Periodicals; Infant Nutrition -- Periodicals; Nutrition Disorders -- Periodicals; Child; 618.923
• DOI: 10.1097/MPG.0000000000002263
• Languages: English
• ISSNs: 0277-2116

Abstract

Abstract : ABSTRACT: Congenital portosystemic shunts are increasingly recognized in several settings and at any age. The following are some of the most common presentations: prenatal ultrasound, neonatal cholestasis, incidental finding on abdominal imaging, or systemic complications such as unexplained cardiopulmonary or neurological disease, or the presence of liver nodules in a noncirrhotic liver. The purpose of the present review is to summarize clinical presentation and current recommendations for management, and highlight areas of future research. Illustrative examples from the veterinary literature complement our current lack of knowledge of this rare malformation often masquerading as a multisystem disease.