A case of tracheobronchomalacia due to relapsing polychondritis treated with Montgomery T-tube. (March 2019)

• Record Type: Journal Article
• Authors: Jeong, Nari; Jang, Hang Jea; Lee, Jae Ha; Kim, Hyeon-Kuk; Park, Jin Han; Lee, Yoo Jin; Park, Bong Soo
• Is Part Of: SAGE open medical case reports. Volume 7(2019)
• Publication Date: 2019-03
• Subjects: Relapsing polychondritis -- tracheobronchomalacia -- tracheostomy; Clinical medicine -- Case studies -- Periodicals; 616.09
• DOI: 10.1177/2050313X19832164
• Languages: English
• ISSNs: 2050-313X

Abstract

Relapsing polychondritis is a rare and multi-system autoimmune disease of unknown etiology characterized by inflammation and destruction of cartilaginous structures. Its clinical manifestations include recurrent chondritis of the ears, nose, pinna, peripheral joints, and laryngotracheobronchial tree and can be life-threatening in advanced cases of laryngotracheal stenosis. Because of the rarity of relapsing polychondritis and lack of understanding of its pathogenesis, there is no standard medical therapy, and treatment is tailored according to disease activity and site of organ involvement. In respiratory failure due to laryngotracheal involvement, which has been reported in up to 50% of relapsing polychondritis patients and is a major cause of death, immediate procedures such as stenting and tracheostomy are very important. This report describes a 70-year-old male patient suffering from tracheobronchomalacia due to relapsing polychondritis who was treated with Montgomery T-tube insertion.