A case and literature review of orbital microcystic adnexal carcinoma. (2nd November 2018)

• Record Type: Journal Article
• Authors: Brent, Alexander J.; Deol, Sundeep S.; Vaidhyanath, Ram; Saldanha, Gerald; Sampath, Raghavan
• Is Part Of: Orbit. Volume 37:Number 6(2018)
• Page Start: 472
• Page End: 475
• Publication Date: 2018-11-02
• Subjects: Microcystic adnexal carcinoma -- radiotherapy -- exenteration; Eye-sockets -- Surgery -- Periodicals; Eye-sockets -- Diseases -- Periodicals; Orbit -- surgery -- Periodicals; Orbital Diseases -- Periodicals; 617.7
• DOI: 10.1080/01676830.2018.1440607
• Languages: English
• ISSNs: 0167-6830

Abstract

ABSTRACT: Microcystic adnexal carcinoma (MAC) is a very rare and locally aggressive sweat gland tumour. MAC has been well reported presenting as a periocular cutaneous lesion, rarely with subsequent direct orbital invasion and only once as a primary orbital lesion. Local recurrence is frequent after primary surgical excision and the role of adjuvant radiotherapy is ill-defined. We describe a case of orbital MAC treated successfully with radiotherapy after incomplete margin clearance post exenteration surgery and review the associated literature.