Comparison of Clinical and Radiological Findings between Congenital Orbital Fibrosis and Congenital Fibrosis of the Extraocular Muscles. (2nd December 2018)

• Record Type: Journal Article
• Authors: Kim, Namju; Yang, Hee Kyung; Kim, Jae Hyoung; Hwang, Jeong-Min
• Is Part Of: Current eye research. Volume 43:Number 12(2018)
• Page Start: 1471
• Page End: 1476
• Publication Date: 2018-12-02
• Subjects: Congenital orbital fibrosis -- congenital fibrosis syndrome -- congenital fibrosis of the extraocular muscles; Ophthalmology -- Periodicals; Eye -- Diseases -- Periodicals; Ophthalmology -- Periodicals; 573.88
• DOI: 10.1080/02713683.2018.1506037
• Languages: English
• ISSNs: 0271-3683

Abstract

ABSTRACT: Purpose/Aims : To compare the clinical and radiological findings of the two rare entities of congenital orbital fibrosis and congenital fibrosis of the extraocular muscles (CFEOM). Materials Methods : Clinical characteristics and magnetic resonance imaging (MRI) findings of three congenital orbital fibrosis patients were analyzed and compared to 13 CFEOM patients. Results : In all three patients with congenital orbital fibrosis, unilateral EOM limitation and enophthalmos were found with a retrobulbar infiltrating mass and normal oculomotor and abducens nerves on MRI. Conversely, most of the patients with CFEOM showed bilateral involvement with hypoplasia of oculomotor nerves and/or abducens nerves and hypotrophic EOM on MRI. Conclusion : All the patients with congenital orbital fibrosis had normal oculomotor and abducens nerves with a retrobulbar mass infiltrating between EOMs, suggesting that congenital orbital fibrosis is a unique disease entity distinguished from CFEOM.