Multiple primary chordomas of the lung. (2018)

• Record Type: Journal Article
• Authors: Ohya, Maki; Yoshida, Kazuo; Shimojo, Hisashi; Shiina, Takayuki
• Is Part Of: Respiratory medicine case reports. Volume 25(2018)
• Page Start: 142
• Page End: 144
• Publication Date: 2018
• Subjects: Chordoma -- Lung -- Brachyury -- Benign notochordal cell tumor; AFP alpha-fetoprotein -- hCG human chorionic gonadotrophin -- BNCT benign notochordal cell tumor -- CEA carcinoembryonic antigen -- CT computed tomography -- FDG-PET fluorine-18 fluorodeoxyglucose positron emission tomography -- H&E hematoxylin and eosin -- IL-2R interleukin-2 receptor; Respiratory organs -- Diseases -- Periodicals; Chest -- Diseases -- Periodicals; Respiratory Tract Diseases -- Periodicals; Respiratory System -- Periodicals; Chest -- Diseases; Respiratory organs -- Diseases; Electronic journals; Periodicals; 616.2
• DOI: 10.1016/j.rmcr.2018.08.012
• Languages: English
• ISSNs: 2213-0071

Abstract

Abstract: We here report the case of a 40-year-old man with primary pulmonary chordomas. Although an abnormality had been noted on a chest radiograph at age 26 years, the patient had not undergone further examination at that time because he was asymptomatic. Standard chest radiographs and computed tomography showed slow-growing, multiple bilateral pulmonary nodules. Two tumors were resected thoracoscopically to obtain a diagnosis. Pathologic examination resulted in a diagnosis of chordomas. Subsequent systemic examination revealed no additional lesions, not even in the axial skeleton. The patient is alive without any new lesions 38 months after surgery. These clinical and pathological findings suggest that our patient has multiple primary chordomas of the lung, which is an extremely rare condition.