Anterior skull base duplication requiring delivery via EXIT procedure: A case report. (December 2018)

• Record Type: Journal Article
• Authors: Shires, Courtney B.; Giurintano, Jonathan P.; McLevy-Bazzanella, Jennifer; Thompson, Jerome
• Is Part Of: International journal of pediatric otorhinolaryngology. Volume 115(2018:Dec.)
• Page Start: 24
• Page End: 26
• Publication Date: 2018-12
• Subjects: EXIT -- Procedure -- Airway; Otolaryngology -- Periodicals; Pediatrics -- Periodicals; Otolaryngology -- Periodicals; Pediatrics -- Periodicals; Oto-rhino-laryngologie -- Périodiques; Pédiatrie -- Périodiques; 618.9209751
• DOI: 10.1016/j.ijporl.2018.09.010
• Languages: English
• ISSNs: 0165-5876

Abstract

Abstract: Duplication of the anterior skull base structures is an extremely rare malformation of failed midline blastogenesis. We present the case of a child with an obstructive oral cavity mass diagnosed on prenatal imaging. The child was successfully delivered by EXIT procedure, a tracheotomy was performed, and postnatal imaging demonstrated an array of craniofacial malformations, including complete duplication of the maxilla, pituitary glands, aqueducts of Sylvius, and basilar arteries. The child underwent excision of the duplicate maxilla, resulting in a wide cleft palate that will be repaired at a future date.