Fistula between the right pulmonary artery and the left atrium coexisting with a secundum‐type atrial septal defect: An unusual case of cyanosis in a girl. Issue 7 (19th June 2019)

• Record Type: Journal Article
• Authors: Zhang, Wei‐Min; Zhu, Hai‐xu; Maimaitiaili, Aizezi; Ayibieke, Naibi; Ermek, Tangsakar; Liu, Jun; Zhang, Zong‐gang; Li, Shi‐guo
• Is Part Of: Echocardiography. Volume 36:Issue 7(2019)
• Page Start: 1423
• Page End: 1426
• Publication Date: 2019-06-19
• Subjects: congenital heart disease -- fistula -- pulmonary artery; Echocardiography -- Periodicals; Echocardiography -- Periodicals; 616.1207543
• DOI: 10.1111/echo.14414
• Languages: English
• ISSNs: 0742-2822

Abstract

Abstract: A fistula between the pulmonary artery (PA) and the left atrium (LA) is a rare congenital heart disease that usually presents with cyanosis, clubbing, and dyspnea, as well as the signs and symptoms of a right‐to‐left shunt. Herein, we report a 16‐year‐old girl with a fistula between the right PA and the LA. This type of fistula could lead to systemic desaturation. This patient also had an atrial septal defect of the secundum type and has been followed up without treatment. The clinical manifestations and treatment of fistulas located between the PA and LA are also reviewed in this report.