Variation factors of stereotypical hand movements in subjects with Rett syndrome. (18th August 2019)

• Record Type: Journal Article
• Authors: Hirano, Daisuke; Taniguchi, Takamichi
• Is Part Of: Developmental neurorehabilitation. Volume 22:Number 6(2019)
• Page Start: 376
• Page End: 379
• Publication Date: 2019-08-18
• Subjects: Hand -- RTT -- SMID -- stereotypy -- upper extremity; Children with disabilities -- Rehabilitation -- Periodicals; Developmentally disabled children -- Rehabilitation -- Periodicals; 615.542
• DOI: 10.1080/17518423.2018.1523245
• Languages: English
• ISSNs: 1751-8423

Abstract

ABSTRACT: Background : Stereotypical hand movements have been observed in most individuals diagnosed with Rett syndrome.Objectives : To investigate factors that increase or decrease hand stereotypies in individuals with Rett syndrome.Methods : A questionnaire regarding hand stereotypies or purposeful hand behaviours was sent to 1016 schools for special needs education and 204 facilities in Japan.Results : Information was acquired from 216 cases (3–53 years old) with Rett syndrome; 81.9% and 87.6% of individuals had factors that increased and decreased stereotypical hand movements, respectively. Stereotypies were mainly increased by displeasure (63.8%) or pleasure (48.5%), and decreased by somnolence (43.5%), pleasure (30.0%), or food (24.1%).Conclusion : Emotion was the main factor increasing stereotypical hand movements, whereas there were a large number of factors that decreased these movements. The factors that decrease stereotypies could be useful to prevent the skin problems or joint contracture observed in patients with Rett syndrome.