Postauricular Melanocytic Neuroectodermal Tumor of Infancy: A Rare Site of a Rare Tumor—MNTI as a Postauricular Mass with Literature Review. (5th July 2018)

• Record Type: Journal Article
• Authors: Evans, S.; Woolley, A.
• Other Names: Morshed Kamal Academic Editor.
• Is Part Of: Case reports in otolaryngology. Volume 2018(2018)
• Publication Date: 2018-07-05
• Subjects: Otolaryngology -- Periodicals; Otolaryngology -- Case studies -- Periodicals; Otolaryngology; Otorhinolaryngologic Diseases; Otolaryngology; Periodicals; Case studies; Periodicals; Case Reports; Fulltext; Internet Resources; Periodicals; 617.51
• DOI: 10.1155/2018/9829856
• Languages: English
• ISSNs: 2090-6765

Abstract

Abstract : Melanocytic neuroectodermal tumor of infancy (MNTI) is a rare osteolytic neoplasm of neural crest cell origin. There are less than 500 documented cases, most frequently affecting the maxilla of infants less than 1 year old. We present a unique case of a two-month-old male with a progressive postauricular mass since birth, confirmed to be a MNTI. The lesion required three resections over the course of five months, with rapid recurrence ultimately requiring a craniectomy, highlighting the difficulty in treating these tumors. Histological and radiographic features were reviewed; an updated literature review for identifying and treating these lesions is presented.