A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements. (26th May 2015)

• Record Type: Journal Article
• Authors: Higashioka, Kazuhiko; Yoshida, Kenji; Oryoji, Kensuke; Kamada, Kazuo; Mizuki, Shinichi; Tsukamoto, Hiroshi; Yokota, Eisuke; Akashi, Koichi
• Other Names: Hsu Tsai-Ching Academic Editor.
• Is Part Of: Case reports in rheumatology. Volume 2015(2015)
• Publication Date: 2015-05-26
• Subjects: Rheumatology -- Periodicals; Rheumatology -- Case studies -- Periodicals; Rheumatic Diseases; Connective Tissue Diseases; Rheumatology; Periodicals; Electronic journals; Case studies; Periodicals; 616.723
• DOI: 10.1155/2015/392893
• Languages: English
• ISSNs: 2090-6889

Abstract

Abstract : We report a case of IgG4-related disease (IgG4-RD) with multiple ten-organ involvement. This case showed many clinical findings, such as bilateral swelling of salivary and lacrimal glands, autoimmune pancreatitis, interstitial nephritis, retroperitoneal fibrosis, periaortitis, systemic swelling of lymph nodes, pulmonary lesions, splenomegaly, and jejunal lesions. He was suspected as having SLE or malignant lymphoma but diagnosed as having IgG4-RD by the elevated serum IgG4 level and histological findings from kidney and lymph node. We report a case of IgG4-RD with multiple ten-organ involvement that was successfully treated with prednisolone therapy.