Primary alveolar rhabdomyosarcoma of retrorectal-presacral space in an adult patient: A case report of an uncommon tumor with rare presentation. Issue 10 (March 2019)

• Record Type: Journal Article
• Authors: Zhu, Xiu-Liang; Su, Wei-Wei; Tang, Jin-Long; Yao, Li-Ding; Lu, Liang-Ji; Sun, Xiu-Juan
• Other Names: NA. section editor.
• Is Part Of: Medicine. Volume 98:Issue 10(2019)
• Publication Date: 2019-03
• Subjects: alveolar -- computed tomography -- magnetic resonance imaging -- retrorectal-presacral space -- rhabdomyosarcoma; Medicine -- Periodicals; Medicine -- Periodicals; Médecine -- Périodiques; Geneeskunde; Medicine; Periodicals; Periodicals; 610.5
• DOI: 10.1097/MD.0000000000013416
• Languages: English
• ISSNs: 0025-7974

Abstract

Abstract: Rationale: Rhabdomyosarcoma (RMS) has known as a highly malignant soft tissue sarcoma, representing 5% to 10% of all solid tumors in childhood. Alveolar rhabdomyosarcoma (ARMS) of the retrorectal-presacral space is an extremely rare lesion for adult, no study has been reported in the English literature. Patient concerns: A 51-year-old male presented with abdominal pain for 1 month, significantly worse when having a bowel movement. Diagnosis: Computed tomography (CT) and magnetic resonance imaging (MRI) of the pelvis showed a solid-cystic, enhancing lesion of dimension located in retrorectal-presacral space. The surgical specimen was reported as ARMS after pathological evaluation. Interventions: The tumor was complete surgical resection, and after surgery, the patient was treated with combination chemotherapy. Outcomes: At 23 months follow up, the patient was asymptomatic with no evidence of metastases or local recurrence. Lessons: Improvements in imaging in addition to early surgical intervention and chemotherapy treatment are crucial to improve survival chances against RMS.