Schnitzler Syndrome: A Dramatic Response to Anakinra. Issue 2 (June 2016)

• Record Type: Journal Article
• Authors: Gouveia, Ana; Micaelo, Manuela; Pierdomenico, Francesca; Freitas, João
• Is Part Of: Dermatology and therapy. Volume 6:Issue 2(2016)
• Page Start: 299
• Page End: 302
• Publication Date: 2016-06
• Subjects: Anakinra -- Schnitzler syndrome -- Urticaria; Dermatologic agents -- Periodicals; Skin -- Diseases -- Treatment -- Periodicals; Dermatology -- Periodicals; Skin Diseases -- Periodicals; Dermatologic Agents -- Periodicals; Dermatologic Surgical Procedures -- Periodicals; 616.506
• DOI: 10.1007/s13555-016-0108-7
• Languages: English
• ISSNs: 2193-8210

Abstract

Abstract Schnitzler syndrome is a rare acquired systemic disease with a chronic evolution and difficult treatment. We report a 50-year-old woman with Schnitzler syndrome for 10 years, with major impact on her quality of life and refractory to conventional therapies. The patient was started on anakinra, an IL-1 receptor antagonist, with a rapid and sustained remission of the syndrome manifestations.