Fontan Revision: Presurgical Planning Using Four-Dimensional (4D) Flow and Three-Dimensional (3D) Printing. Issue 2 (March 2019)

• Record Type: Journal Article
• Authors: Carberry, Thomas; Murthy, Raghav; Hsiao, Albert; Petko, Colin; Moore, John; Lamberti, John; Hegde, Sanjeet
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 10:Issue 2(2019)
• Page Start: 245
• Page End: 249
• Publication Date: 2019-03
• Subjects: pulmonary arteriovenous malformations -- Fontan -- 3D printing -- 4D flow -- magnetic resonance imaging (MRI); Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135118799641
• Languages: English
• ISSNs: 2150-1351

Abstract

Pulmonary arteriovenous malformations (AVMs) can be a complication of certain postoperative Fontan patients whose hepatic venous blood return is not distributed evenly to both lungs. A ten-year-old female, who had previously undergone staged single ventricle palliation for complex congenital heart disease, underwent a Fontan revision due to significant left-sided pulmonary AVMs and increasing arterial oxygen desaturation. The combination of four-dimensional flow cardiac magnetic resonance imaging and three-dimensional printing enabled presurgical planning for a Fontan takedown and diversion of hepatic venous flow to the azygous vein that resulted in significant clinical improvement.