A giant aggressive angiomyxoma of vulva in a young woman: A case report. Issue 2 (January 2019)

• Record Type: Journal Article
• Authors: Xie, Yao; Qian, Yanping; Zou, Bingyu
• Other Names: NA. section editor.
• Is Part Of: Medicine. Volume 98:Issue 2(2019)
• Publication Date: 2019-01
• Subjects: aggressive angiomyxoma -- vulva -- mesenchymal tumor; Medicine -- Periodicals; Medicine -- Periodicals; Médecine -- Périodiques; Geneeskunde; Medicine; Periodicals; Periodicals; 610.5
• DOI: 10.1097/MD.0000000000013860
• Languages: English
• ISSNs: 0025-7974

Abstract

Abstract: Rationale: Aggressive angiomyxoma (AAM) is a rare and benign invasive mesenchymal stromal tumor predominantly in women at reproductive age. AAM tends to relapse locally and should be differentially diagnosed from other mesenchymal tumors. Patient concerns: We report here a rare case of massive vulvar AAM in a 22-year-old Chinese woman with left labia majora mass with ulcer. Diagnoses: The diagnosis "aggressive angiomyxoma of vulva" was based on clinicopathologic and immunohistochemical features. Interventions: A surgery with local excision of the mass was performed. Outcomes: The patient was discharged 12 days after the surgery. There was no AAM recurrence or metastasis in a period of 12-month follow-up. Lessons: The vulvar AAM is a benign and aggressive mesenchymal tumor. In this case, we present the diagnosis, treatment, and prognosis for vulvar AAM. The tumor was removed completely by the surgery, but a long-term follow-up is requisite for surveilling on recurrence.