Amelanocytic anorectal malignant melanoma—Case report. (2019)

• Record Type: Journal Article
• Authors: Serra, Marta; Santos, Teresa; Martins, Margarida; Sardo, Leonor
• Is Part Of: International journal of surgery case reports. Volume 55(2019)
• Page Start: 164
• Page End: 167
• Publication Date: 2019
• Subjects: AMM anorectal malignant melanoma -- APR abdominoperineal resection -- CT computed tomography -- ER emergency room -- HIV human immunodeficiency virus -- HPV human papilomavirus -- PET positron emission tomography -- RLL right lower lobe -- WLE wide local excision; Anorectal malignant melanoma -- Amelanocytic -- Surgery -- Wide local excision -- Abdominal perineal resection -- Case report; Surgery -- Periodicals; Surgical Procedures, Operative -- Periodicals; Surgery; Electronic journals; Periodicals; 617.005
• DOI: 10.1016/j.ijscr.2019.01.029
• Languages: English
• ISSNs: 2210-2612

Abstract

Highlights: Anorectal malignant melanoma, is a rare and aggressive form of melanoma. Very different from its cutaneous counterpart. There is no optimal treatment. Surgery is the mainstay of treatment, but the extent is controversial. Patient's quality of life deserves attention when choosing the adequate surgical technic. Abstract: Introduction: Anorectal malignant melanoma (AMM), is a rare and aggressive form of melanoma. Accounts for <2% of melanomas, and <2% of anal tumors. It is more frequent at the 6 th –7 th decade, mostly in women. Surgery is the mainstay of treatment, but the extent is controversial. Case presentation: 82-year-old male, presented with rectal mass in the Emergency Room (ER). After local excision, pathology observed that the mass corresponded to AMM. Despite being stage I (Local disease), a year later it presented with local recurrence and distant metastasis. The patient died 32 months after diagnosis. Conclusions: There is no optimal treatment, due to the lack of prospective studies. Wide local excision (WLE) has faster recovery, less post-operatory complications and similar survival rate compared to abdominal perineal resection (APR).