A case report on Herlyn–Werner–Wunderlich syndrome with spontaneous abortion. Issue 36 (September 2018)

• Record Type: Journal Article
• Authors: Jia, Guifeng; Chai, Wei; Cui, Miao; Wen, Yan; Cui, Lifeng; Gong, Fengyan
• Other Names: NA. section editor.
• Is Part Of: Medicine. Volume 97:Issue 36(2018)
• Publication Date: 2018-09
• Subjects: abortion -- Herlyn–Werner–Wunderlich syndrome -- pregnancy -- renal agenesis -- uterus didelphys; Medicine -- Periodicals; Medicine -- Periodicals; Médecine -- Périodiques; Geneeskunde; Medicine; Periodicals; Periodicals; 610.5
• DOI: 10.1097/MD.0000000000012004
• Languages: English
• ISSNs: 0025-7974

Abstract

Abstract: Introduction: Herlyn–Werner–Wunderlich syndrome (HWWS) is a rare congenital abnormality of the urogenital tract characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It is usually diagnosed after menarche, with a clinical presentation of dysmenorrhea, recurrent abdominal pain, and irregular menses. However, it is rare to diagnose it during pregnancy, subsequently resulting in spontaneous abortion. Case presentation: A 22-year-old Chinese woman with HWWS whose left uterine pregnancy underwent spontaneous abortion presented with a right perforated obstructed hemivagina and right renal agenesis. The right vaginal septum was resected and the hematocolpos was drained, thereby relieving lower abdominal pain and preserving future fertility. Conclusion: Co-presentation of unilateral renal agenesis and uterus didelphys should encourage clinicians to rule out HWWS. Early diagnosis and subsequent treatment can avoid possible serious complications.