Spontaneous Compartment Syndrome in a Patient with McArdle Disease: A Case Report and Review of the Literature. Issue 3 (July 2017)

• Record Type: Journal Article
• Authors: Triplet, Jacob J.; Goss, David A.; Taylor, Benjamin
• Is Part Of: JBJS case connector. Volume 7:Issue 3(2017)
• Publication Date: 2017-07
• Subjects: Orthopedic surgery -- Case studies -- Periodicals; Orthopedic surgery -- Periodicals; Orthopedics; Orthopedic Procedures; Orthopedic surgery; Periodicals; Electronic journals; Case studies; Periodicals; 616.7
• DOI: 10.2106/JBJS.CC.16.00196
• Languages: English
• ISSNs: 2160-3251

Abstract

Abstract : Case: McArdle disease, a glycogen storage disorder, often manifests as exercise intolerance secondary to muscle ischemia. Few authors have reported on rhabdomyolysis or compartment syndrome following inciting events among patients with McArdle disease. We present the case of a 40-year-old woman who developed spontaneous compartment syndrome of the right forearm and subsequently underwent emergency fasciotomy. Conclusion: On the basis of the present case and our review of the current literature, we advocate a high level of suspicion for compartment syndrome in patients with a history of McArdle disease.