Bladder Perivascular Epithelioid Cell Tumor (PEComa): A Case Report and Literature Review. Issue 2 (April 2015)

• Record Type: Journal Article
• Authors: Sarti, Alessandra; Rubilotta, Emanuele; Balzarro, Matteo; Cerruto, Maria Angela; Brunelli, Matteo; Artibani, Walter
• Is Part Of: Urologia journal. Volume 82:Issue 2(2015)
• Page Start: 120
• Page End: 123
• Publication Date: 2015-04
• Subjects: Perivascular epithelioid cell tumor -- PEComa -- Bladder -- TURBT -- Cystectomy; Urology -- Periodicals; 616.6005
• DOI: 10.5301/urologia.5000045
• Languages: English
• ISSNs: 0391-5603

Abstract

Introduction: Perivascular epithelioid cell tumors (PEComa) are a very uncommon mesenchymal cancer with uncertain malignant potential. Materials and Methods: A computerized research on Pub Med was performed regarding bladder PEComa. We evaluated the literature cases and described a case of bladder PEComa. Results: PEComa of the bladder is a very rare neoplasm and only 15 cases have been reported so far. Conclusions: Bladder PEComa involves young subjects of both genders, mostly under 40 years of age. Surgical treatment (partial or radical cystectomy) is the most common management. A long-term follow-up and larger series are required to better understand the best clinical approach to bladder PEComa.