Retroperitoneal Liposarcomas: A Representative Literature Review Occasioned by a Rare Case of Laterelapse Abdominal Liposarcoma. Issue 2 (April 2016)

• Record Type: Journal Article
• Authors: Pisani, Michela; Al-Buheissi, Salah; Whittlestone, Tim
• Is Part Of: Urologia journal. Volume 83:Issue 2(2016)
• Page Start: 68
• Page End: 70
• Publication Date: 2016-04
• Subjects: Abdominal liposarcomas -- Late-relapse liposarcomas -- Liposarcoma tumours -- Liposarcomas -- Soft-tissue sarcomas -- Urological liposarcomas; Urology -- Periodicals; 616.6005
• DOI: 10.5301/uro.5000142
• Languages: English
• ISSNs: 0391-5603

Abstract

Soft tissue sarcomas (STS) are rare and heterogeneous tumours representing approximately 0.7%-1% of all adult tumours. In the adults and among the retroperitoneal sarcomas (RPS), Liposarcoma (LS) is the most common variant accounting for 12% −20% of all sarcomas and up to 45% of sarcomas at retroperitoneal localization. A rare case of LS relapsed after 15 years is giving the occasion to review the published literature and emphasise the followings concepts: 1) Despite extensive surgery remains the mainstay of treatment for localized STS at present, anatomical complexity and occult localization result in local recurrence in the majority of patients; 2) The role of imaging and tumour markers is still limited; 3) Indefinite prolonged surveillance is a key point of treatment; 4) Referral to tertiary centres with dedicated Retroperitonal Surgeons and Oncology expertise is mandatory.