Adult-onset Still's disease with prominent polyserositis. Issue 2 (May 2018)

• Record Type: Journal Article
• Authors: Farooq Sheikh, Ali Sibtain; Marks, Jonathan; Hopkinson, Neil
• Is Part Of: Scottish medical journal. Volume 63:Issue 2(2018)
• Page Start: 63
• Page End: 66
• Publication Date: 2018-05
• Subjects: Adult-onset Still's disease -- anaemia -- pericarditis -- pleural effusion -- pyrexia of unknown origin; Medicine -- Periodicals; 610.5
• DOI: 10.1177/0036933018760763
• Languages: English
• ISSNs: 0036-9330

Abstract

Adult-onset Still's disease is a systemic autoinflammatory disease the presentation of which can often mimic infection. As a consequence, there is often a delay in diagnosis. Serositis is a recognised but less common clinical feature that can result in complications including cardiac tamponade and constrictive pericarditis. We describe a case of adult-onset Still's disease without the hallmark rash or significant arthritis, presenting with polyserositis that showed a good response to initial steroid treatment and sustained remission with anakinra. An elevated procalcitonin level was due to active adult-onset Still's disease, not bacterial infection.