Assessing the prevalence of juvenile systemic sclerosis in childhood using administrative claims data from the United States. Issue 2 (June 2018)

• Record Type: Journal Article
• Authors: Beukelman, Timothy; Xie, Fenglong; Foeldvari, Ivan
• Is Part Of: Journal of scleroderma and related disorders. Volume 3:Issue 2(2018)
• Page Start: 189
• Page End: 190
• Publication Date: 2018-06
• Subjects: Prevalence -- juvenile systemic sclerosis; Scleroderma (Disease) -- Periodicals; Systemic scleroderma -- Periodicals; Fibrosis -- Periodicals; 616.544
• DOI: 10.1177/2397198318763701
• Languages: English
• ISSNs: 2397-1983

Abstract

Juvenile systemic sclerosis is a very rare orphan disease. To date, only one publication has estimated the prevalence of juvenile systemic sclerosis using a survey of specialized physicians. We conducted a study of administrative claims data in the United States using the International Classification of Diseases, Ninth Revision diagnosis codes and found a prevalence of approximately 3 per 1, 000, 000 children. This estimate will inform the planning of prospective studies.