Focal Nodulary Hyperplasia of the Liver Due to Congenital Portosystemic Shunt: A Rare Condition Mimicking Hepatocellulary Carcinoma. Issue 1 (January 2017)

• Record Type: Journal Article
• Authors: Yazal Erdem, Arzu; Emir, Suna; Demir, Haci A.; Özyörük, Derya; Çetin, İlker; Turan, Aynur; Karakuş, Esra
• Is Part Of: Journal of pediatric hematology/oncology. Volume 39:Issue 1(2017)
• Publication Date: 2017-01
• Subjects: focal nodulary hyperplasia -- congenital portosystemic shunt; Pediatric hematology -- Periodicals; Tumors in children -- Periodicals; 618.9215
• DOI: 10.1097/MPH.0000000000000666
• Languages: English
• ISSNs: 1077-4114

Abstract

Abstract : Congenital portosystemic shunts are rare vascular malformations that lead to several complications including liver tumors, pulmonary hypertension, and metabolic encephalopathy. We describe a rare case of a 17-year-old girl with an extrahepatic portosystemic shunt presenting recurrent syncope episodes and a liver mass mimicking hepatocellulary carcinoma.