Autoimmune Pancreatitis Type 2: Case Report. (October 2017)

• Record Type: Journal Article
• Authors: Onweni, Chidinma; Balagoni, Harika; Treece, Jennifer M.; Addo Yobo, Emmanuel; Patel, Archi; Phemister, Jennifer; Srinath, Manoj; Young, Mark F.
• Is Part Of: Journal of investigative medicine high impact case reports. Volume 5:Number 4(2017)
• Publication Date: 2017-10
• Subjects: autoimmune pancreatitis -- type 1 -- type 2 -- corticosteroid therapy -- IgG4 antibody -- IgG4-related disease -- chronic pancreatitis -- lymphoplasmacytic sclerosing pancreatitis; Internal medicine -- Periodicals; Medical care -- Periodicals; 616.005
• DOI: 10.1177/2324709617734245
• Languages: English
• ISSNs: 2324-7096

Abstract

A middle-aged man presents with acute pancreatitis of unknown etiology and is found to have a presentation consistent with the diagnosis of type 2 autoimmune pancreatitis (AIP). AIP is a group of rare heterogeneous diseases that are challenging to diagnose. There are 2 types of AIP. Type 1 disease is the more common worldwide than type 2 AIP. While type 1 AIP is associated with IgG4-positive antibodies, type 2 AIP is IgG4 antibody negative. Both types of AIP are responsive to corticosteroid treatment. Although type 1 AIP has more extrapancreatic manifestations and more commonly relapses, this is a case of a patient with type 2 AIP with inflammatory bowel disease and relapsing course.