Prenatal physiologic findings and postnatal advanced imaging in the management of absent pulmonary valve syndrome with intact ventricular septum. Issue 10 (13th August 2018)

• Record Type: Journal Article
• Authors: Cadiz, Emilia Maria C.; Pasierb, Michele M.; Dolgner, Stephen J.; Arya, Bhawna
• Is Part Of: Echocardiography. Volume 35:Issue 10(2018)
• Page Start: 1695
• Page End: 1697
• Publication Date: 2018-08-13
• Subjects: cardiac imaging -- congenital heart disease -- diagnostic imaging tools -- pulmonary valve; Echocardiography -- Periodicals; Echocardiography -- Periodicals; 616.1207543
• DOI: 10.1111/echo.14121
• Languages: English
• ISSNs: 0742-2822

Abstract

Abstract : Absent pulmonary valve syndrome is a congenital heart defect usually associated with tetralogy of Fallot. Rarely, absent pulmonary valve syndrome can occur independently of tetralogy of Fallot and presents with an intact ventricular septum and a patent ductus arteriosus. This case report describes the prenatal diagnosis of absent pulmonary valve syndrome with intact ventricular septum via echocardiogram and the postnatal management of the resulting physiologic effects secondary to this rare congenital heart disease.