Normocephalic Pancraniosynostosis: A Report of a Surgical Technique. Issue 5 (July 2017)

• Record Type: Journal Article
• Authors: Czerwinski, Marcin; Monsivais, Sharon
• Is Part Of: Journal of craniofacial surgery. Volume 28:Issue 5(2017)
• Publication Date: 2017-07
• Subjects: Craniosynostosis -- multisuture -- normocephalic pancraniosynostosis -- pancraniosynostosis; Facial bones -- Surgery -- Periodicals; Skull -- Surgery -- Periodicals; Face -- Surgery -- Periodicals; Surgery, Plastic -- Periodicals; 617.52
• DOI: 10.1097/SCS.0000000000003638
• Languages: English
• ISSNs: 1049-2275

Abstract

Abstract : Abstract: Normocephalic pancraniosynostosis is defined as the premature fusion of 3 or, more major sutures in the absence of another primary etiology, including primary, microcephaly, ventriculoperitoneal shunting, hypothyroidism, rickets, mucopolysaccharidoses, or other lysosomal storage diseases. It is very rare, thus far only 6 patients have been reported in the literature. Patients tend to present much later than those with single sutural, synostoses, and up to half have evidence of elevated intracranial pressure. The authors wish to present another patient, with emphasis on a unique treatment approach.