Modified Aortic Uncrossing Procedure: A Novel Approach for Norwood Palliation of Complex Univentricular Congenital Heart Disease With a Circumflex Aorta. (July 2017)

• Record Type: Journal Article
• Authors: Bryant, Roosevelt; Wallen, William; Rizwan, Raheel; Morales, David L.
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 8:Number 4(2017)
• Page Start: 507
• Page End: 510
• Publication Date: 2017-07
• Subjects: congenital heart surgery -- CHD -- univentricular heart -- aortic arch -- Norwood procedure; Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135117712248
• Languages: English
• ISSNs: 2150-1351

Abstract

The circumflex aorta is a rare type of true vascular ring anomaly. It consists of a retroesophageal right aortic arch, a left-sided descending thoracic aorta, and a left-sided ligamentum arteriosum. The "aortic uncrossing procedure" described by Planché and Lacour-Gayet is the procedure of choice for managing this aortic anomaly in patients with a biventricular heart. The presence of a circumflex aorta in a patient with heterotaxy syndrome and univentricular congenital heart disease requiring Norwood palliation is highly unusual. We report such a case and describe our approach to its surgical management.