Perioperative and Anesthetic Considerations in Total Anomalous Pulmonary Venous Connection. (June 2017)

• Record Type: Journal Article
• Authors: Ross, Faith J.; Joffe, Denise; Latham, Gregory J.
• Is Part Of: Seminars in cardiothoracic and vascular anesthesia. Volume 21:Number 2(2017:Jun.)
• Page Start: 138
• Page End: 144
• Publication Date: 2017-06
• Subjects: total anomalous pulmonary venous return -- congenital heart disease -- cardiac anesthesia -- intraoperative assessment -- postoperative complications; Cardiovascular system -- Surgery -- Methods -- Periodicals; Chest -- Surgery -- Methods -- Periodicals; Anesthesia -- Periodicals; Anesthetics -- Periodicals; Anesthesia -- Periodicals; Anesthetics -- Periodicals; Cardiovascular Surgical Procedures -- methods -- Periodicals; Thoracic Surgical Procedures -- methods -- Periodicals; 617.96
• DOI: 10.1177/1089253216672012
• Languages: English
• ISSNs: 1089-2532

Abstract

Total anomalous pulmonary venous connection (TAPVC) is a potentially devastating form of congenital heart disease in which all pulmonary blood flow returns to the systemic venous circulation rather than the left atrium. Anomalous pulmonary venous flow may be obstructed at birth, and affected infants present with severe cyanosis and poor cardiac output unresponsive to standard resuscitation with prostaglandin. Obstructed TAPVC remains one of the few indications for emergent neonatal cardiac surgery. This review will discuss the physiology and perioperative management of isolated TAPVC without associated cardiac lesions.