A systematic surgical approach to hepatoblastoma with intracardiac extension. (May 2017)

• Record Type: Journal Article
• Authors: Sayed, Sajid; Prabhu, Sudesh; Fawcett, Jonathan; Choo, Kelvin; Alphonso, Nelson
• Is Part Of: Asian cardiovascular & thoracic annals. Volume 25:Number 4(2017)
• Page Start: 300
• Page End: 303
• Publication Date: 2017-05
• Subjects: Chemotherapy -- adjuvant -- Cardiopulmonary bypass -- Heart right atrium -- Hepatoblastoma -- Induced deep hypothermia -- Liver neoplasms; Heart -- Diseases -- Asia -- Periodicals; Heart -- Diseases -- Pacific Area -- Periodicals; Heart -- Diseases -- Periodicals; Heart -- Surgery -- Asia -- Periodicals; Heart -- Surgery -- Pacific Area -- Periodicals; Heart -- Surgery -- Periodicals; Chest -- Surgery -- Asia -- Periodicals; Chest -- Surgery -- Pacific Area -- Periodicals; Chest -- Surgery -- Periodicals; 617.412
• DOI: 10.1177/0218492317705565
• Languages: English
• ISSNs: 0218-4923

Abstract

Hepatoblastoma is very uncommon in children, and intracardiac extension is rare. The SIOPEL-4 regime for metastatic hepatoblastoma has extended the surgical options with good results. We successfully treated a boy aged 2 years and 9 months with hepatoblastoma, using a multidisciplinary surgical strategy involving an extended left hepatectomy, left adrenalectomy, biopsy of the paraaortic and coeliac lymph nodes, and resection of the inferior vena caval-right atrial extension of the hepatoblastoma, under cardiopulmonary bypass and deep hypothermia.