Late‐onset severe long QT syndrome. Issue 4 (30th November 2017)

• Record Type: Journal Article
• Authors: Asatryan, Babken; Schaller, André; Bartholdi, Deborah; Medeiros‐Domingo, Argelia
• Is Part Of: Annals of noninvasive electrocardiology. Volume 23:Issue 4(2018:Jul.)
• Page Start: n/a
• Page End: n/a
• Publication Date: 2017-11-30
• Subjects: channelopathy -- genetic test -- long QT syndrome -- sudden death; Electrocardiography -- Periodicals; Arrhythmia -- Periodicals; 616.1207547
• DOI: 10.1111/anec.12517
• Languages: English
• ISSNs: 1082-720X

Abstract

Abstract : We report a case of torsades de pointes arrhythmia as the first manifestation of congenital Long QT syndrome in a 77‐year‐old man with family history of sudden unexplained death. This case illustrates the importance of vigilant clinical assessment and genetic counseling in families with sudden death in order to identify properly asymptomatic relatives at risk for cardiac events. It also demonstrates that Long QT syndrome can still manifest with potentially fatal arrhythmias late in life in previously asymptomatic elderly patients.