Primary hyperoxaluria: Orthodontic management in a pediatric patient: A case report. (8th June 2018)

• Record Type: Journal Article
• Authors: Cazzolla, A. P.; Zhurakivska, K.; Ciavarella, D.; Lacaita, M. G.; Favia, G.; Testa, N. F.; Marzo, G.; La Carbonara, V.; Troiano, G.; Lo Muzio, L.
• Is Part Of: Special care in dentistry. Volume 38:Number 4(2018)
• Page Start: 259
• Page End: 265
• Publication Date: 2018-06-08
• Subjects: orthodontics -- pediatric dentistry -- rare disorders; People with disabilities -- Dental care -- Periodicals; Older people -- Dental care -- Periodicals; Hospital dental service -- Periodicals; Dental Care for Disabled -- Periodicals; Dental Service, Hospital -- Periodicals; Geriatric Dentistry -- Periodicals; 617.60087
• DOI: 10.1111/scd.12302
• Languages: English
• ISSNs: 0275-1879

Abstract

Abstract: Aims: The aim of this study is to report the case of the orthodontic treatment in a patient affected by primary hyperoxaluria type 1 and subjected to a combinate liver‐kidney transplant. Methods and results: The 9‐year patient was admitted to our department for the presence of facial dysmorphism. The patient was affected by primary hyperoxaluria type 1 and has undergone a combined liver‐kidney transplantation. At the time of the visit, he was in treatment with immunosuppressive drugs and received a corticosteroid and an antibiotic therapy monthly. An intraoral and extraoral examination, as well as radiographic and model analysis, was performed in order to define an accurate diagnosis and a proper rehabilitation planning. An orthopedic‐orthodontic treatment was performed and satisfactory final results obtained. A laser gingivectomy was also realized for eliminate the gengival hyperplasia probably induced by cyclosporine assumption. Both skeletal and dental relationships were improved by the treatment, reaching a good dental arches alignment. Conclusion: An early diagnosis, as well as a multidisciplinary approach, is very important in patients with rare diseases. An appropriate treatment allowed us to achieve acceptable results and improve the patient quality of life.