A case of extensive acquired progressive lymphangioma. Issue 4 (6th April 2018)

• Record Type: Journal Article
• Authors: Larkin, Sydney C.; Wentworth, Ashley B.; Lehman, Julia S.; Tollefson, Megha M.
• Is Part Of: Pediatric dermatology. Volume 35:Issue 4(2018)
• Page Start: 486
• Page End: 489
• Publication Date: 2018-04-06
• Subjects: acquired progressive lymphangioma -- benign lymphangioendothelioma -- lymphangioma -- sirolimus; Pediatric dermatology -- Periodicals; Children -- Diseases -- Periodicals; 618.925
• DOI: 10.1111/pde.13486
• Languages: English
• ISSNs: 0736-8046

Abstract

Abstract: Acquired progressive lymphangioma (benign lymphangioendothelioma) is a rare lymphatic anomaly of unclear pathogenesis. Excision is generally advised for local disease, although other therapies have been tried. This report describes a unique case of extensive acquired progressive lymphangioma involving the abdomen, genitalia, and lower extremity of a 1‐year‐old boy. Rapid progression and multisite involvement required exploration of nonsurgical options for management.