A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites. Issue 6 (17th April 2018)

• Record Type: Journal Article
• Authors: Al Zaki, Alaa A.; Mann, Shawna L.; Carruthers, Mollie N.; Slack, Graham W.; Chen, Luke Y. C.
• Is Part Of: Clinical case reports. Volume 6:Issue 6(2018)
• Page Start: 1098
• Page End: 1100
• Publication Date: 2018-04-17
• Subjects: IgG4‐related disease -- inflammation -- lymphangioma -- steroid; Medicine -- Periodicals; 616.09
• DOI: 10.1002/ccr3.1536
• Languages: English
• ISSNs: 2050-0904

Abstract

Key Clinical Message: Lymphangiomas are benign tumors of the lymphatic vessels, which can be inflammatory and occasionally steroid‐responsive. IgG4‐related disease (IgG4‐RD) is a recently defined fibro‐inflammatory condition. We describe a novel association between reactive IgG4+ plasma cells and cystic lymphangioma in a young woman who had a dramatic clinical response to steroids. Abstract : Lymphangiomas are benign tumors of the lymphatic vessels, which can be inflammatory and occasionally steroid‐responsive. IgG4‐related disease (IgG4‐RD) is a recently defined fibro‐inflammatory condition. We describe a novel association between reactive IgG4+ plasma cells and cystic lymphangioma in a young woman who had a dramatic clinical response to steroids.