An unusual clinical presentation of myxoid dermatofibrosarcoma protuberans with a prominent vasculature: A potential pitfall in the diagnosis of myxoid soft tissue tumors. (23rd March 2018)

• Record Type: Journal Article
• Authors: Tran, Patrick; Henderson, Gregory P.; McLemore, Michael
• Is Part Of: Journal of cutaneous pathology. Volume 45:Number 6(2018)
• Page Start: 419
• Page End: 422
• Publication Date: 2018-03-23
• Subjects: dermatofibrosarcoma protuberans (DFSP) -- myxoid -- myxoid dermatofibrosarcoma -- protuberans -- scalp -- soft tissue; Skin -- Diseases -- Periodicals; Dermatology -- Periodicals; 616
• DOI: 10.1111/cup.13130
• Languages: English
• ISSNs: 0303-6987

Abstract

Abstract : Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue tumor that arises primarily on the trunk and extremities but seldom on the scalp. Several variants of DFSP have been described, including myxoid DFSP. Although typical DFSP may have focally myxoid areas, myxoid DFSP, in which most of the stroma is myxoid, is rare and can pose diagnostic challenges. Here, we report a case of myxoid DFSP with an unusual clinical presentation that could have been mistaken for a lipoma. Additionally, the myxoid DFSP displayed prominent vasculature in a myxoid stroma, which could have been mistaken for a myxoid liposarcoma.