Hypoplastic left heart in Turner's syndrome: a primary indication for transplant?. (13th December 2017)

• Record Type: Journal Article
• Authors: Philip, Joseph; Gupta, Dipankar; Bleiweis, Mark S.; Pietra, Biagio A.; Vyas, Himesh V.
• Is Part Of: Cardiology in the young. Volume 28:Number 3(2018)
• Page Start: 458
• Page End: 460
• Publication Date: 2017-12-13
• Subjects: Turner's syndrome, -- hybrid palliation, -- heart transplant, -- hypoplastic left heart syndrome; Pediatric cardiology -- Periodicals; 618.9212
• DOI: 10.1017/S1047951117001962
• Languages: English
• ISSNs: 1047-9511

Abstract

Abstract: Survival for hypoplastic left heart syndrome patients following the Norwood procedure is 71–90%. Mortality in patients with Turner's syndrome and hypoplastic left heart syndrome after conventional palliation (Norwood operation) has been reported as high as 80%. This questions the approach of traditional staged palliation. Here, we report a patient with hypoplastic left heart syndrome and Turner's syndrome bridged to orthotopic heart transplantation following a hybrid procedure.