Unusual Outcome of a Right Ventricular Rhabdomyoma in an Infant. (May 2016)

• Record Type: Journal Article
• Authors: Lefort, Bruno; Lothion, Julie; Arid, Jean-Marc El; Tabareau-Delalande, Flore; Nassimi, Alaeddin; Neville, Paul; Chantepie, Alain
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 7:Number 3(2016)
• Page Start: 397
• Page End: 399
• Publication Date: 2016-05
• Subjects: cardiac tumors (includes myxoma -- primary -- metastases) -- echocardiography -- infant -- surgery -- emergency; Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135115593133
• Languages: English
• ISSNs: 2150-1351

Abstract

Rhabdomyomas are the most common benign cardiac tumors. They may often be associated with tuberous sclerosis. In many cases, cardiac rhabdomyomas undergo spontaneous regression. Here, we report the unusual case of an infant with a large nonobstructive right ventricular rhabdomyoma at birth and at four months of age, which subsequently caused severe right ventricle outflow tract obstruction at six months of age, prompting surgery to remove the tumor. Close monitoring should be done in infants with large nonobstructive cardiac rhabdomyomas.