Functionally Univentricular Heart With Right Atrial Isomerism and Mixed Total Anomalous Pulmonary Venous Drainage. (May 2016)

• Record Type: Journal Article
• Authors: Talwar, Sachin; Agarwal, Palkesh; Choudhary, Shiv Kumar; Airan, Balram
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 7:Number 3(2016)
• Page Start: 377
• Page End: 380
• Publication Date: 2016-05
• Subjects: total anomalous pulmonary venous connection -- atrial isomerism -- heterotaxy; Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135115590457
• Languages: English
• ISSNs: 2150-1351

Abstract

Patients with right atrial isomerism and total anomalous pulmonary venous connection (TAPVC) in a functionally univentricular heart are a challenging subset with a high mortality rate. We present the case of a patient with univentricular heart who had right atrial isomerism and associated mixed TAPVC (supracardiac, cardiac, and infracardiac). The anatomy was delineated precisely, and the patient underwent first-stage univentricular palliation consisting of TAPVC repair and bilateral bidirectional superior cavopulmonary anastomosis.