Microcystic adnexal carcinoma of the orbit mimicking pagetoid sebaceous gland carcinoma. (4th May 2018)

• Record Type: Journal Article
• Authors: Mukherjee, Bipasha; Subramaniam, Nirmala; Kumar, Krishna; Nivean, Pratheeba Devi
• Is Part Of: Orbit. Volume 37:Number 3(2018)
• Page Start: 235
• Page End: 237
• Publication Date: 2018-05-04
• Subjects: Exenteration -- microcystic adnexal carcinoma -- pagetoid -- sebaceous gland carcinoma; Eye-sockets -- Surgery -- Periodicals; Eye-sockets -- Diseases -- Periodicals; Orbit -- surgery -- Periodicals; Orbital Diseases -- Periodicals; 617.7
• DOI: 10.1080/01676830.2017.1383472
• Languages: English
• ISSNs: 0167-6830

Abstract

ABSTRACT: Microcystic adnexal carcinoma (MAC) is a rare malignancy of sweat glands that has been reported most often on the face in the form of a cutaneous lesion, with the potential for deeper invasion. The synonyms of MAC include sclerosing sweat duct carcinoma, syringomatous carcinoma, and malignant syringoma. Clinically, MAC in the periocular area has been misdiagnosed as basal cell carcinoma, squamous cell carcinoma, or even chalazia. We report a case of MAC presenting clinically as sebaceous gland carcinoma with pagetoid spread for the first time in literature.