Pleomorphic Hyalinizing Angiectatic Tumor Arising in the Hand: A Case Report. (September 2016)

• Record Type: Journal Article
• Authors: Kane, Patrick M.; Gaspar, Michael P.; Whiting, Benjamin B.; Culp, Randall W.
• Is Part Of: Hand. Volume 11:Number 3(2016)
• Page Start: NP20
• Page End: NP23
• Publication Date: 2016-09
• Subjects: pleomorphic hyalinizing angiectatic tumor -- mass -- hand; Hand -- Surgery -- Periodicals; Hand -- Surgery; Periodicals; 617.57005
• DOI: 10.1177/1558944715627275
• Languages: English
• ISSNs: 1558-9447

Abstract

Background: Background: Pleomorphic hyalinizing angiectatic tumors (PHATs) are extremely rare, non-metastasizing tumors of uncertain origin that are typically seen in the lower extremities. To date, it is estimated that less than 100 cases have been reported worldwide since first described in 1996.Methods: The case of a 35-year-old male with a several-year history of a dorsal hand mass is presented. Although the patient was initially asymptomatic, in the months prior to presentation, the patient complained of pain with power grasp and direct pressure over the mass. The patient underwent uncomplicated surgical excision, during which the mass was noted to be adherent to the underlying extensor tendons.Results: Immunopathology confirmed the mass to be PHAT. We believe this is the first documented case of this rare tumor occurring in the hand.Conclusions: History and epidemiology of PHAT are reviewed. Then, in the context of the presented case, pre-operative evaluation, surgical management, pathologic findings and post-operative follow-up are all discussed.