Congenital Erythropoietic Porphyria With Calcific Constrictive Pericarditis: A Case Report and Brief Review of Literature. (October 2015)

• Record Type: Journal Article
• Authors: Chowdhury, Ujjwal K.; Patel, Kartik; Seth, Sandeep; Ray, Ruma; Jagia, Priya; Sahu, Manoj
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 6:Number 4(2015:Oct.)
• Page Start: 646
• Page End: 649
• Publication Date: 2015-10
• Subjects: porphyria -- calcification -- pericardium; Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135115581384
• Languages: English
• ISSNs: 2150-1351

Abstract

An 18-year-old boy with congenital erythropoietic porphyria and calcific constrictive pericarditis underwent total pericardiectomy. The cause of pericardial calcification could be deposition of porphyrins in the pericardium. Surgical importance of this rare condition is highlighted.