Cardiac involvement in Erdheim- Chester disease: MRI findings and literature revision. (7th September 2015)

• Record Type: Journal Article
• Authors: Ponsiglione, Andrea; Puglia, Marta; Barbuto, Luigi; Solla, Raffaele; Altiero, Michele; Lubrano, Valentina; Imbriaco, Massimo
• Is Part Of: Acta radiologica open. Volume 4:Number 9(2015)
• Publication Date: 2015-09-07
• Subjects: Erdheim-Chester disease -- histiocytosis -- non-Langerhans -- cardiac magnetic resonance; Radiology -- Periodicals; Diagnostic Imaging -- Periodicals; Radiology; Periodicals; 616.075705
• DOI: 10.1177/2058460115592273
• Languages: English
• ISSNs: 2058-4601

Abstract

Erdheim-Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis, characterized by the involvement of several organs. The lesions may be skeletal or extra-skeletal: in particular, long bones, skin, lungs, and the cardiovascular and the central nervous systems can be affected. In this report, we describe a case of a 34-year-old man, who came to our observation with symptomatic ECD, for a correct assessment of the degree of cardiac involvement through magnetic resonance imaging (MRI).