Pulmonary artery aneurysm and sarcoidosis. (January 2015)

• Record Type: Journal Article
• Authors: Gerloni, Riccardo; Merlo, Marco; Vitrella, Giancarlo; Lardieri, Gerardina; Pinamonti, Bruno; Pappalardo, Aniello; Cattin, Luigi; Sinagra, Gianfranco
• Is Part Of: Journal of cardiovascular medicine. Volume 16(2015)Supplement 2
• Publication Date: 2015-01
• Subjects: cardiac magnetic resonance -- cardiac sarcoidosis -- pulmonary artery aneurysm; Cardiology -- Periodicals; Cardiovascular system -- Diseases -- Periodicals; Cardiology -- Periodicals; Cardiovascular Diseases -- Periodicals; 616.1005
• DOI: 10.2459/JCM.0b013e328365a04f
• Languages: English
• ISSNs: 1558-2027

Abstract

Abstract : Pulmonary artery aneurysm unassociated to congenital heart disease and pulmonary hypertension is exceedingly rare. Its pathogenesis and correct management remain unknown. Sarcoidosis is a systemic disease that can exceptionally involve large vessels, leading to stenosis and dilatation. Pulmonary artery aneurysm has never been described in association with sarcoidosis. Surgical approach should prevent aneurysm rupture, but it is not known when surgery should be preferred to strict medical follow-up. In this report we present a case of large pulmonary artery aneurysm associated to systemic sarcoidosis underlining problematic management of diseases 'forgotten' by evidence based medicine.